Idiopathic pulmonary fibrosis

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aka Usual Interstital Pneumonia (UIP)


  • Basal and peripheral reticular opacities
  • Honeycombing
  • Traction bronchiectasis
  • Apicobasal gradient - gets worse from apex to base
  • Limited ground glass opacities
  • Heterogeneous - diseased lung alternating with healthy lung
  • Exclusion of known causes (toxins, environmental exposure, etc)
  • No treatment available


UIP1.jpg
UIP2.jpg
UIP3.jpg