Heterotaxy

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Malrotation
Polysplenia

Heterotaxy is the disordered organ arrangement in the chest or abdomen, aka situs ambiguous. Radiographic finding of clinical significance include malrotation, congenital heart diseasea and asplenia. Congenital heart disease in 50-100%.


Situs solitus is the usual arrangement of organs and vessels within the body.


Situs inversus describes a mirror image of situs solitus. Effects 0.1% of population and has a 5% association with congential heart disease.


Kartagener syndrome: situs inversus, nasal polyps, chronic sinusitis and bronchiectasis (caused by immobile cilia).


Polysplenia: left isomerism or bilateral left sidedness.


Asplenia: right isomerism or bilateral right sidedness, both lungs have three lobes.


Article

Situs Revisited: Imaging of the Heterotaxy Syndrome