Cystic fibrosis

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CFcxr.jpg
CFct.jpg
  • Autosomal recessive
  • Caucasians
  • 1/2000 live births
  • Viscous lung secretions
  • Common infections, pseudomonas, staph aureus
  • Cystic bronchiectasis, plugged bronchus, mosaic perfusion
  • Meconium ileus